The full Klüver-Bucy syndrome (KBS) – hyperorality, placidity, hypermetamorphosis, dietary changes, altered sexual behavior, and visual. Klüver-Bucy syndrome is a very rare cerebral neurological disorder associated with damage to both temporal lobes resulting in abnormalities in memory, social . Klüver-Bucy syndrome is described here because its cause is usually bilateral lesions in the territory of the PCAs. In the small number of reports of the syndrome .

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Sgndrome disorder Impulse control disorder Kleptomania Trichotillomania Pyromania Dermatillomania Factitious disorder Munchausen syndrome. Social neurosciences research shows that changes in temporal lobe is identified as a cause for aberrant sexual and hyper-sexual behaviors. The Kluver-Bucy syndrome is a clinical syndrome observed in humans and other animals after bilateral lesions in the temporal lobe that involve the amygdala, hippocampal formation, and adjacent neural structures.

Adjustment disorder with depressed mood. Adult personality and behavior Gender dysphoria Sexual maturation disorder Ego-dystonic sexual orientation Sexual relationship disorder Paraphilia Voyeurism Fetishism. Korsakoff syndrome is a deficiency of vitamin B-1 that leads to cardiovascular, central and peripheral nervous system disturbances.

Schizoaffective disorder Schizophreniform disorder Brief reactive psychosis. Retrieved from ” https: For information about clinical trials sponsored syndromw private sources, contact: While this cluster of syndromes is common to such sources as ‘s The Neuropsychiatry of Limbic and Subcortical Disorders’s Functional Neuroanatomy: Bergman; Ronald Arly Bergman Rage, Power, and Aggression.


Slaughter J, et al. D ICD – The Neuropsychiatry of Limbic and Subcortical Disorders.

Frontotemporal degeneration is a very rare progressive neurological disease initially predominately affecting the frontal and temporal lobes of the brain. Together we are strong.

The Klüver-Bucy Syndrome.

Some current clinical trials also are posted on the following page on the NORD website: Principles of Neurology, 6th ed. Sapolsky, who addresses the syndrome and iluver associated legal significance of neurological defenses.

Disorganized hebephrenic schizophrenia Paranoid schizophrenia Simple-type schizophrenia Childhood schizophrenia Pseudoneurotic schizophrenia. Human cases were recognized in the s, as surgeons employed bilateral temporal lobectomies to treat seizures.

Comparisons may be useful for a differential diagnosis:.

Rare Disease Database

The clinical features of KBS in man are similar to those in monkeys, but the full syndrome is rarely seen, probably because the anterior temporal lobe dysfunction is usually less severe than that following total temporal lobe ablation sybdrome monkeys.

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Various attempts were made to localize the component features to specific areas of the temporal lobe, with mixed success. Human KBS does not occur in isolation, but is typically part of a complex behavioral syndrome that almost always includes amnesia and aphasia, and that may also include dementia and seizures.


Later symptoms are principally cardiovascular and neurological. Sexual maturation disorder Ego-dystonic sexual orientation Sexual relationship disorder Paraphilia Voyeurism Fetishism.

About News Events Contact. It is characterized by progressive deterioration of intellect with changes in behavior and personality.

However, in later stages there is loss of motor control as well as confusion and severe dementia. This page was last edited on 27 Decemberat Produced by Pat Iluver. Box Bethesda, MD Phone: An almost uncontrollable appetite for food may also be noted.

All studies receiving U. There may also be other symptoms associated with dementia loss of reason as well. X-linked intellectual disability Lujan—Fryns mluver.

Comparisons may be useful for a differential diagnosis: Disorders typically diagnosed in childhood Intellectual disability X-linked intellectual disability Lujan—Fryns syndrome. Mental disorders due to a general medical condition Sexual arousal Syndromes affecting the nervous system Amygdala Psychopathological syndromes Rare syndromes.