Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis. Images in Clinical Medicine from The New England Journal of Medicine — Heerfordt’s Syndrome, or Uveoparotid Fever. Heerfordt’s syndrome is a rare manifestation of sarcoidosis characterized by the presence of facial nerve palsy, parotid gland enlargement.

Author: Nar Arakus
Country: Turkey
Language: English (Spanish)
Genre: Love
Published (Last): 19 December 2015
Pages: 288
PDF File Size: 3.36 Mb
ePub File Size: 15.35 Mb
ISBN: 623-2-86195-808-4
Downloads: 57364
Price: Free* [*Free Regsitration Required]
Uploader: Sasho

Given the patient’s acute onset of unilateral facial droop, the differential diagnosis includes vascular, infectious, granulomatous, neoplastic, and autoimmune causes of cranial nerve VII injury Table 1.

As uveitis and BHL had been previously diagnosed, she underwent a syndroje examination for sarcoidosis in the Department of Respiratory Medicine in our hospital.

The Heerfordt-Waldenström syndrome as an initial presentation of sarcoidosis

Radiologic manifestations of sarcoidosis in various organs. Loading Stack – 0 images remaining.

About Blog Go ad-free. Treatment depends on the severity of systemic impairment. Chest, lung, abdominal, and extremity exams were unremarkable. Computed tomography CT of the chest showed hilar lymphadenopathy with bibasilar interstitial lung disease.


Epidemiology Clinical presentation Radiographic features Treatment and prognosis History and etymology Practical points Related articles References. National Center for Biotechnology InformationU. This article has been cited by other articles in PMC.

The Heerfordt-Waldenström syndrome as an initial presentation of sarcoidosis

Heerfordt syndrome with unilateral facial nerve palsy: CT of the neck soft tissues demonstrating prominent cervical lymphadenopathy. His symptoms were improved by corticosteroid heerfodt. The condition was first described in by Danish ophthalmologist Christian Frederick Heerfordt, for whom the syndrome is now named.

Sarcoidosis is a granulomatous disease of unclear etiology, which commonly presents with cough, dyspnea, chest pain, fever, weight loss, arthralgias, and erythema nodosum.

CT of the neck soft tissues demonstrated enlarged lymph nodes, the largest of which measured 3. Synonyms or Alternate Spellings: Find articles by Larissa Karine Leite Portocarrero. Find articles by Neusa Yuriko Sakai Valente. Support Center Support Center. Treatments for sarcoidosis include corticosteroids and immunosuppressive drugs. By using this site, you agree to the Terms of Use and Privacy Policy. The likelihood of permanent paralysis increases in patients who are not treated with corticosteroids.

A pure tone audiogram showed normal hearing and stapedial reflex on the right side was normal. As he also presented with a 3-month history of swelling of the right parotid gland and a 1-month history of right facial palsy, he heeerfordt referred to the Department of Otolaryngology.


Orofacial presentations of sarcoidosis—a case series and review of the literature.

The exact cause of Heerfordt syndrome has not yet been definitively determined. Unable to process the form.

Larissa Karine Leite Portocarrero, Av. PET showed hypermetabolic activity in the bilateral hilar lymph nodes, mediastinal lymph nodes, lung, spleen, and myocardium Figure 5.

Case Reports in Otolaryngology

Presence of multinucleated cells in the granuloma right photo, hematoxylin and eosin, X This patient had marked improvement of symptoms after 4 days of prednisone therapy. Support Center Support Center. Support Radiopaedia and see fewer syndeome. Introduction Sarcoidosis is a systemic granulomatous disease of unknown etiology.

Esophagogastroduodenoscopy showed pharyngeal edema but no evidence of obstruction.